pericardial effusion in langerhans cell histiocytosis: a case report

نویسندگان

narges gholami assistant professor of pediatrics, loghman hakim hospital, shahid beheshti university of medical sciences, tehran, ir iran; assistant professor of pediatrics, loghman hakim hospital, shahid beheshti university of medical sciences, tehran, ir iran. tel: +98-2155419005, fax: +98-2155417547

چکیده

conclusions pericardial effusion was a rare finding in this case of langerhans cell histiocytosis. pericardial effusion in langerhans cell histiocytosis, which is an unusual presentation, should be considered when the patient experiences respiratory distress. introduction langerhans cell histiocytosis (lch) is a proliferative disorder of histiocytes in multiple organs. langerhans cell histiocytosis involves bones, skin, lung and other organs. case presentation this study describes a seven-month-old iranian girl who presented with skin rash and cervical lymphadenopathy. langerhans cell histiocytosis was suspected when it was associated with anemia, splenomegaly and lytic bone lesions. a skin biopsy confirmed the diagnosis of langerhans cell histiocytosis. during hospitalization, the patient looked ill with respiratory distress. a chest x-ray showed a ground glass view, and echocardiography showed moderate pericardial effusion.

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عنوان ژورنال:
iranian red crescent medical journal

جلد ۱۸، شماره ۶، صفحات ۰-۰

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